nidНефрология и диализNephrology and Dialysis1680-44222618-9801Российское диализное обществоnid-1314Research ArticleНАБЛЮДЕНИЯ ИЗ ПРАКТИКИCASE REPORTSИнфантильный нефротический синдром у ребенка с олигонефронией и дизгенезией гонадInfantile nephrotic syndrome in a child with oligonephronia and gonadal dysgenesisПриходинаЛ. С.PrikhodinaL. S.prikhodina@rambler.ruАгаповЕ. Г.AgapovE. G.noemail@neicon.ruНевструеваВ. В.NevstruevaV. V.noemail@neicon.ruТурпиткоО. Ю.TurpitkoO. Yu.noemail@neicon.ruЗверевД. В.ZverevD. V.noemail@neicon.ruКаабакМ. М.KaabakM. M.noemail@neicon.ruДлинВ. В.DlinV. V.noemail@neicon.ruИгнатоваМ. С.IgnatovaM. S.noemail@neicon.ruФГУ «МНИИ педиатрии и детской хирургии Росмедтехнологий»Russian FederationДетский Центр гравитационной хирургии крови и гемодиализаRussian FederationРоссийский научный центр хирургии РАМН; г. МоскваRussian Federation2008190620251016772Copyright © Приходина Л.С., Агапов Е.Г., Невструева В.В., Турпитко О.Ю., Зверев Д.В., Каабак М.М., Длин В.В., Игнатова М.С., 20252025Приходина Л.С., Агапов Е.Г., Невструева В.В., Турпитко О.Ю., Зверев Д.В., Каабак М.М., Длин В.В., Игнатова М.С.Prikhodina L.S., Agapov E.G., Nevstrueva V.V., Turpitko O.Y., Zverev D.V., Kaabak M.M., Dlin V.V., Ignatova M.S.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nephro.ru/jour/article/view/1314

Представлены результаты клинического наблюдения ребенка с инфантильным нефротическим синдромом при олигонефронии в сочетании с дизгенезией гонад, характеризующимся прогрессирующим течением с развитием терминальной хронической почечной недостаточности в дошкольном возрасте. Описана дифференциальная диагностика ряда состояний, протекающих с инфантильным нефротическим синдромом, анализируется патогенез олигонефронии, приводятся этапы наблюдения и терапии пациента в зависимости от состояния почечных функций.

The paper presents the results of a follow-up of a child with infantile nephrotic syndrome with oligonephronia and gonadal disgenesis, which progressed to end stage renal disease at the preschool age. This paper describes the differential diagnosis of various conditions associated with infantile nephrotic syndrome, pathogenesis of oligonephronia, the stages of the follow-up and treatment according to the patent’s renal function.

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The authors declare that there are no conflicts of interest present.