nidНефрология и диализNephrology and Dialysis1680-44222618-9801Российское диализное общество10.28996/2618-9801-2026-2-123-186nid-4006Research ArticleСтатьиКлинические практические рекомендации KDIGO 2025 по ведению иммуноглобулин А нефропатии (IgA-Н) и иммуноглобулин A васкулита (IgA-В). Перевод на русский язык Е.В. Паршиной, Н.М. Буланова и А.А. Ефимовой под редакцией Е.В. ЗахаровойKDIGO 2025 Clinical Practice Guideline for the Management of Immunoglobulin A Nephropathy (IgAN) and Immuno­globulin A Vasculitis (IgAV). Translated into Russian by E.V. Parshina, N.M. Bulanov and A.A. Efimova, edited by E.V. ZakharovaРедакционнаястатьяEditorialArticle202629062026282123186Copyright © Редакционная с., 20262026Редакционная с.Editorial a.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nephro.ru/jour/article/view/4006

Клинические практические рекомендации KDIGO («Инициативы по Улучшению Глобальных Исходов Заболеваний Почек») 2025 по ведению иммуноглобулин A нефропатии (IgA-Н) и иммуноглобулин A васкулита (IgA-В) представляют целенаправленное обновление Главы 2 Клинических практических рекомендаций KDIGO по ведению гломерулярных заболеваний 2021, посвященной иммуноглобулин A нефропатии (IgA-Н) / иммуноглобулин A васкулиту (IgA-В). Их основная цель – помочь врачам, оказывающим помощь лицам с IgA-Н или IgA-В. В ходе подготовки нового варианта были учтены результаты рандомизированных контролируемых исследований, опубликованных с апреля 2023 года, с обновлением в августе 2024 года. Как и в 2021 году, рекомендации представляют руководство по диагностике, оценке прогноза, лечению и действиям в особых ситуациях. Будучи основано на новой доказательной базе, это обновление преимущественно сфокусировано на рекомендациях, относящихся к IgA-Н. Разработка этих рекомендаций стала результатом детального анализа и оценки доказательной базы. Подходы к лечению и рекомендации основаны на систематическом обзоре релевантных исследований и оценке убедительности доказательной базы и силы рекомендаций по системе “Оценки, разработки и оценивания рекомендаций” (GRADE). В рекомендациях обсуждаются ограничения доказательной базы, а также представлены направления будущих исследований.

The Kidney Disease: Improving Global Outcomes (KDIGO) 2025 Clinical Practice Guideline for the Management of Immunoglobulin A Nephropathy (IgAN) and Immunoglobulin A Vasculitis (IgAV) represents a focused update of Chapter 2: Immunoglobulin A Nephropathy (IgAN) / Immunoglobulin A Vasculitis (IgAV) from the KDIGO 2021 Clinical Practice Guideline for the Management of Glomerular Diseases. The aim is to assist healthcare providers caring for people with IgAN or IgAV. The update takes into consideration evidence from randomized controlled trials published through April 2023 and updated in August 2024. As in 2021, this guideline provides guidance related to diagnosis, prognosis, treatment, and special situations. Based on the new evidence, this update is mostly related to the guidance relevant to IgAN. Development of this guideline followed an explicit process of evidence review and appraisal. Treatment approaches and guideline recommendations are based on systematic reviews of relevant studies, and appraisal of the certainty of the evidence and the strength of recommendations following the “Grading of Recommendations Assessment, Development and Evaluation” (GRADE) approach. Limitations of the evidence are discussed, and areas of future research are also presented.

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The authors declare that there are no conflicts of interest present.