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Hematuria in hereditary nephropathies

Abstract

Isolated hematuria in hereditary nephropathies is characterized on the basis of literature data and our own experience. An attention was focused on the thin basement membrane disease (TBMD) and the Alport syndrome because these diseases have different prognosis. It is pointed out that TBMD could be a predisposition factor in the development of immune glomerulopathies. Preliminary results of therapy of the Alport syndrome with ACE-inhibitors are presented

About the Author

M. S. Ignatova
ФГУ МНИИ педиатрии и ДХ Росздрава, г. Москва
Russian Federation


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Review

For citations:


Ignatova M.S. Hematuria in hereditary nephropathies. Nephrology and Dialysis. 2006;8(4):363-369. (In Russ.)

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