Infantile nephrotic syndrome in a child with oligonephronia and gonadal dysgenesis
Abstract
The paper presents the results of a follow-up of a child with infantile nephrotic syndrome with oligonephronia and gonadal disgenesis, which progressed to end stage renal disease at the preschool age. This paper describes the differential diagnosis of various conditions associated with infantile nephrotic syndrome, pathogenesis of oligonephronia, the stages of the follow-up and treatment according to the patent’s renal function.
About the Authors
L. S. Prikhodina
ФГУ «МНИИ педиатрии и детской хирургии Росмедтехнологий»
Russian Federation
Russian Federation
E. G. Agapov
ФГУ «МНИИ педиатрии и детской хирургии Росмедтехнологий»
Russian Federation
Russian Federation
V. V. Nevstrueva
ФГУ «МНИИ педиатрии и детской хирургии Росмедтехнологий»
Russian Federation
Russian Federation
O. Yu. Turpitko
ФГУ «МНИИ педиатрии и детской хирургии Росмедтехнологий»
Russian Federation
Russian Federation
D. V. Zverev
Детский Центр гравитационной хирургии крови и гемодиализа
Russian Federation
Russian Federation
M. M. Kaabak
Российский научный центр хирургии РАМН; г. Москва
Russian Federation
Russian Federation
V. V. Dlin
ФГУ «МНИИ педиатрии и детской хирургии Росмедтехнологий»
Russian Federation
Russian Federation
M. S. Ignatova
ФГУ «МНИИ педиатрии и детской хирургии Росмедтехнологий»
Russian Federation
Russian Federation
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Review
For citations:
Prikhodina L.S., Agapov E.G., Nevstrueva V.V., Turpitko O.Yu., Zverev D.V., Kaabak M.M., Dlin V.V., Ignatova M.S. Infantile nephrotic syndrome in a child with oligonephronia and gonadal dysgenesis. Nephrology and Dialysis. 2008;10(1):67-72. (In Russ.)
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