Pancytopenia and hemophagocytic syndrome after kidney transplantation (Review of the literature with case report)
Abstract
Hemophagocytic syndrome (HFS) is a rare life-threatening syndrome that is characterized by fever, splenomegaly, pancytopenia and the presence of hemophagocytosis in bone marrow and other tissues. The review summarizes recent data on pathogenesis, clinical presentation and treatment of HFS. We also present a case of fatal infection-associated HFS in a renal transplant recipient.
About the Authors
E. I. Prokopenko
Московский областной научно-исследовательский клинический институт им. М.Ф. Владимирского
Russian Federation
Russian Federation
E. O. Scherbakova
Московский областной научно-исследовательский клинический институт им. М.Ф. Владимирского
Russian Federation
Russian Federation
A. V. Vatazin
Московский областной научно-исследовательский клинический институт им. М.Ф. Владимирского
Russian Federation
Russian Federation
S. U. Gulimova
Московский областной научно-исследовательский клинический институт им. М.Ф. Владимирского
Russian Federation
Russian Federation
A. P. Martynyuk
Московский областной научно-исследовательский клинический институт им. М.Ф. Владимирского
Russian Federation
Russian Federation
V. B. Banina
Московский областной научно-исследовательский клинический институт им. М.Ф. Владимирского
Russian Federation
Russian Federation
L. E. Gaganov
Московский областной научно-исследовательский клинический институт им. М.Ф. Владимирского
Russian Federation
Russian Federation
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Review
For citations:
Prokopenko E.I., Scherbakova E.O., Vatazin A.V., Gulimova S.U., Martynyuk A.P., Banina V.B., Gaganov L.E. Pancytopenia and hemophagocytic syndrome after kidney transplantation (Review of the literature with case report). Nephrology and Dialysis. 2010;12(2):082-089. (In Russ.)
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